| 증례 / 간동정맥 단락을 동반한 유전성 출혈성 모세관 확장증 1례 ( A Case of Hereditary Hemorrhagic Telangiectasia ) |
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| A Case of Hereditary Hemorrhagic Telangiectasia |
| Ji Kyum Kim, M.D., Sung Ho Park, M.D., Ki Hun Kim, M.D., Ho Jong Seo, M.D. Kwang Suk Kim, M.D.,
Jin Wook Choi, M.D., Ho Jung Kim, M.D., Tae Seob Choi, M.D., Hae Kyung Kim,* M.D.
and Jong Suk Kim,* M.D. |
| Department of Internal Medicine, Sung-Ae General Hospital, Seoul, Korea
*Department of Internal Medicine, KwangMyung-SungAe General Hospital, KwangMyung, Korea |
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| ABSTRACT |
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Hereditary hemorrhagic telangiectasia (HHT ) is an autosomal dominant inherited disease
characterized by telangiectasias of the skin , mucou s membranes, and various organ sy stem. HHT is
not unusual in western countries but there were several reported cases of HHT in Korea. Recently
we evaluated a 40- year - old postpartum female who had been suffering from recurrent epistaxis and
peripartum dyspnea. T he patient was diagnosed as a HHT complicated by high output heart failure
caused by intrahepatic arteriovenous malformation. This case is reported with a review of relevant
literature.(Korean J Hepatol 2000 ;6 :5 14 - 5 18) |
| KeyWords:
Hereditary hemorrhagic telangiectasia, Intrahepatic arteriovenous malformation |
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