증례 : 간을 침범한 소아에서의 특발성 과호산구성 증후군 ( Case Reports : A Case of Idiopathic Hypereosinophilic Syndrome with Hepatic Involvement in a 5 - Year - Old Boy ) |
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A Case of Idiopathic Hypereosinophilic Syndrome with Hepatic Involvement in a 5 - Year - Old Boy |
Young Mi Kim, M.D., Yoon Jin Lee, M.D., Jae Hong Park, M.D.,
Jun Woo Lee, M.D.1, and Chang Hun Lee, M.D.2 |
Department of Pediatrics, Radiology1 and Pathology2, College of Medicine, Pusan National University, Pusan, Korea |
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ABSTRACT |
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Idiopathic hypereosinophilic syndrome is defined as the presence of prolonged eosinophilia without an identifiable underlying cause and with evidence of end-organ dysfunction. The organs involved are the heart, bone marrow, nervous system, lungs, liver, skin, and gastrointestinal tract. Hepatic involvement is found in about 30% of patients of idiopathic hypereosinophilic syndrome. It occurs rarely in infants and children. In this report, we experienced one case of idiopathic hypereosinophilic syndrome with hepatic involvement in a 5-year-old boy who complained of intermittent fever and right upper quadrant abdominal pain. An abdominal ultrasound examination revealed an ill-defined low-echoic lesion in the liver. Pathologic findings of a biopsy specimen clearly showed the infiltration of eosinophils in the liver. Laboratory data disclosed absolute eosinophilia. There was no evidence of allergic disease or parasitic infestation. (Korean J Hepatol 2002;8:321-326) |
KeyWords:
Idiopathic hypereosinophilic syndrome, Hepatic involvement |
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